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Key medical literature
The published sources behind this site. Where possible we link to a version you can read in full; otherwise to the publication record. This is information and does not replace your specialist.
1.Della-Torre E, Talarico R, Ballarin J, et al. The five red flags for IgG4-related disease. The Lancet Rheumatology, 2025.
Read source2.Wallace ZS, Naden RP, Chari S, et al. The 2019 ACR/EULAR classification criteria for IgG4-related disease. Arthritis & Rheumatology, 2020.
Read source3.Wallace ZS, Katz G, Hernandez-Barco YG, Baker MC. Current and future advances in practice: IgG4-related disease. Rheumatology Advances in Practice, 2024.
Read source4.Iaccarino L, Talarico R, Scire CA, et al. IgG4-related diseases: state of the art on clinical practice guidelines. RMD Open, 2019.
Read source5.Sina S, Bonisoli GL, et al. Clinicopathological pearls and diagnostic pitfalls in IgG4-related disease. Diagnostics, 2025.
Read source6.Maritati F, Peyronel F, Vaglio A. IgG4-related disease: a clinical perspective. Rheumatology, 2020.
Read source7.Abraham M, Khosroshahi A. Diagnostic and treatment workup for IgG4-related disease. Expert Review of Clinical Immunology, 2017.
Read source8.Khosroshahi A, Wallace ZS, Crowe JL, et al. International consensus guidance statement on the management and treatment of IgG4-related disease. Arthritis & Rheumatology, 2015.
Read source9.Stone JH, et al. Inebilizumab for treatment of IgG4-related disease. New England Journal of Medicine, 2025.
Read source10.Cagnotto G, Backlund RT, Bengtsson A, Bruschettini M. Immunosuppressants for IgG4-related disease (protocol). Cochrane Database of Systematic Reviews, 2025.
Read source11.Cuéllar MC, et al. Enfermedad relacionada a IgG4. Serie clínica de pacientes chilenos. Rev Med Chile 2022;150:705-710.
Read source12.Martínez Calabuig P, et al. Enfermedad relacionada con IgG4: revisión de casos diagnosticados entre 2010-2021. Rev. Sociedad Val. Reuma. 2022;8(5):4-10.
Read source13.Lanzillotta M, Campochiaro C, Mancuso G, et al. Clinical phenotypes of IgG4-related disease reflect different prognostic outcomes. Rheumatology (Oxford) 2020;59:2435-2442.
Read source14.Okazaki K (ed.). IgG4-Related Disease. Current Topics in Microbiology and Immunology, vol. 401. Springer International Publishing, 2017.
Read source15.Orozco Gálvez O. Enfermedad relacionada con la IgG4: creación de un algoritmo diagnóstico y terapéutico europeo y nuevas técnicas de medicina nuclear. Doctoral thesis, Universitat Autònoma de Barcelona, 2024.
Read source16.Bateman AC, Culver EL. Challenges and pitfalls in the diagnosis of IgG4-related disease. Seminars in Diagnostic Pathology, 2023.
Read source17.Reisch M, Spindelböck WJ, Hodl I, et al. Azathioprine as maintenance therapy for IgG4-related diseases: a retrospective case series and case-based review of the literature. Rheumatology International, 2026.
Read source18.González-García A, Starita-Fajardo G, Lucena López D, Iranzo Alcolea MP, et al. New Developments in the Treatment of IgG4-Related Disease: A Comprehensive Clinical Approach. J Clin Med 2025;14(19):6774 (literature searched through July 2025).
Read source19.Peyronel F, Della-Torre E, Maritati F, Urban ML, Bajema I, Schleinitz N, Vaglio A. IgG4-related disease and other fibro-inflammatory conditions. Nat Rev Rheumatol 2025;21(5):275-290.
Read source20.Stone JH. IgG4-related disease: lessons from the first 20 years. Rheumatology (Oxford) 2025;64(Suppl 1):i24-i27.
Read source21.Arias-Intriago M, Gomolin T, Jaramillo F, et al. IgG4-Related Disease: Current and Future Insights into Pathological Diagnosis. Int J Mol Sci 2025;26(11):5325.
Read source22.Khurram SA, Gueiros LAM, Soares CD, Fonseca FP. IgG4-Related Disease. In: Lymphoproliferative and Granulomatous Disorders of the Oral Cavity. Springer, 2025:207-213.
Read source23.Hao Q, Lian D, Zhou M, et al. Identification of candidate biomarkers for diagnosis, disease activity, and relapse prediction in IgG4-related disease. Arthritis Res Ther, 2026.
Read source24.Stone JH, et al. Obexelimab for IgG4-related disease (INDIGO trial). N Engl J Med, published online 2 June 2026.
Read source25.Duru N, van der Goes MC, Jacobs JWG, et al. EULAR evidence-based and consensus-based recommendations on the management of medium to high-dose glucocorticoid therapy in rheumatic diseases. Ann Rheum Dis 2013;72(12):1905-1913.
Read source26.Fong AC, Cheung NW. The high incidence of steroid-induced hyperglycaemia in hospital. Diabetes Res Clin Pract 2013.
Read source27.Nuthalapati M, Menon AR, Rajendran R, et al. IgG4-Related Disease in Urological Practice: A Case Series of Mistaken Malignancies. Indian J Surg Oncol 2025;16(6):1446-1451.
Read source28.Tomkins M, Martin-Grace J, Kennedy C, et al. Adrenal insufficiency is common amongst kidney transplant recipients receiving maintenance prednisolone and can be predicted using morning cortisol. Nephrol Dial Transplant 2023;38(2):236-245.
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National clinical guidance
The links below point outside this site, to help you look further on your own. We do not control or endorse them, and we gain nothing from listing them. Unlike our own sources above, these are not checked by us for origin or accuracy. Always confirm anything important with your specialist.
1.Protocole National de Diagnostic et de Soins (PNDS), Maladie associee aux IgG4, Haute Autorite de Sante, FAI2R and CERAINOM-IgG4, November 2025.
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Product information (regulatory)
The links below point outside this site, to help you look further on your own. We do not control or endorse them, and we gain nothing from listing them. Unlike our own sources above, these are not checked by us for origin or accuracy. Always confirm anything important with your specialist.
1.Ficha técnica prednisona, Agencia Española de Medicamentos y Productos Sanitarios (AEMPS), CIMA
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Useful websites
The links below point outside this site, to help you look further on your own. We do not control or endorse them, and we gain nothing from listing them. Unlike our own sources above, these are not checked by us for origin or accuracy. Always confirm anything important with your specialist.
- European Federation for IgG4-related disease
- IgG4ward! Foundation
- IgG4ward! Academy (online learning course)
- Asociación Española de Pacientes con Enfermedad Relacionada con IgG4 (AE-IgG4)
- Association Française du Syndrome et de la maladie associée aux IgG4 (AFRIGG4)
- Orphanet, the portal for rare diseases
